DICER1 and ovarian sex cord-stromal tumor: However, these participants and their relatives (especially children and female individuals) are at risk for a set of well-characterized DICER1-associated tumors that can be prospectively identified and managed33 with established DICER1-specific surveillance guidelines.34 Such surveillance is particularly appealing (and, with subsequent interventions, potentially curative) for highly morbid DICER1-associated tumors, such as PPB and ovarian sex-cord stromal tumors.