Noticeably, we previously identified TCERG1 as a partner protein of huntingtin and a polymorphic repeat DNA (encoding an imperfect (Gln-Ala)(38) tract) in TCERG1 as a potential modifier of HD onset (Holbert et al., 2001) whose expression rescues striatal cell death in lentiviral overexpression (rats) and knock-in (mouse cells) models of mutant huntingtin neurotoxicity (Arango et al., 2006). Here, TCERG1 is linked to Huntington disease.