In our population, two heterozygous missense VUSs in COL6A3 gene (c.1214T>C) and FKTN gene (c.-7C>G) were reported in a 61-year-old male with NM with sinus bradycardia, first degree AV block, and right axis deviation in ECG, as well as LVH in TTE. This evidence concerns the gene COL6A3 and nemaline myopathy.