TNPO3 and limb-girdle muscular dystrophy: Moreover, miR-206 have been described to significantly increase in patients affected by LGMD D2, a dominant form of LGMD due to a mutation in the TNPO3 gene; the described increase could open a new perspective for this myomiRNA as biomarker of disease severity and evolution in LGMD D2 patients [Pegoraro V et al. 2020, To be submitted].