However, TDP-43 microvasculopathy has been described in 3 cases with familial FTLD-TDP type A, one case with familial Lewy body disease, and one case with Perry syndrome, both with accompanying TDP-43 proteinopathy; TDP-43 vasculopathy is rarely encountered in the cerebral cortex in TDP-43 types B and C (54, 55). Here, TARDBP is linked to Perry syndrome.