Among WNT family members, mutations in WNT10A (OMIM ∗606268) are predominantly related to tooth agenesis (TA) involving both nonsyndromic/isolated/selective tooth agenesis (NSTA/STHAG4, MIM #150400) and syndromic tooth agenesis, such as odontoonychodermal dysplasia (MIM #257980) and Schopf-Schulz-Passarge syndrome (MIM #224750). Here, WNT10A is linked to Schöpf-Schulz-Passarge syndrome.