Contrary to our study in which three of four patients who tested positive for pathogenic SDHB variants had urogenital PGL, a Korean study of 2 patients with pathogenic SDHB variants did not report any urogenital paraganglioma involvement [30]; instead, both patients presented with adrenal pheochromocytoma with one of them behaving in a malignant manner. Here, SDHB is linked to paraganglioma.