Autosomal-dominant-subtypes were less common with 3 laminopathies (EDMD2; 3%), 1 myotilinopathy (Myofibrillar Myopathy; 1%), and 1 HSP40-proteinopathy (LGMDD1 DNAJB6-related; 1%). The gene discussed is DNAJB6; the disease is proteostasis deficiencies.