In investigating anti-DFS70 positive patients with SARD, half of the anti-DFS70 positive pediatric patients were diagnosed with SARD including 9 JIA (22.5%, 9/40), 8 undifferentiated connective tissue disease (UCTD) (20.0%, 8/40) and 3 SLE (7.5%, 3/40) while anti-DFS70 positive. Here, PSIP1 is linked to systemic lupus erythematosus.