Two cases of KCNQ1OT1 LOM with adrenocortical tumors also recently observed (Wijnen et al., 2012), and an additional one recently reported, although neither of these patients presented typical phenotypic features of BWS (Wijnen et al., 2012; Eltan et al., 2020). This evidence concerns the gene KCNQ1OT1 and adrenal cortex neoplasm.