Cystic Fibrosis (CF; OMIM 219700) is an autosomal recessive disorder caused by mutations in the gene coding the cystic fibrosis transmembrane conductance regulator (CFTR) which functions as a chloride and bicarbonate-permeable ion channel protein in the apical cell membranes of various epithelia, including the lungs, pancreas, and sweat glands (1, 2). Here, CFTR is linked to cystic fibrosis.