Carbamyl phosphate synthetase (CPS) deficiency, Ornithine transcarbamylase (OTC) deficiency, Argininosuccinate synthetase (AS) deficiency, Argininosuccinate lyase (AL) deficiency, Arginase deficiency?, Nacetyl glutamate synthetase deficiency. This evidence concerns the gene ASS1 and hyperinsulinemic hypoglycemia, familial, 4.