POMC and Aarskog-Scott syndrome, X-linked: Familial glucocorticoid deficiency (FGD) (OMIM #202200), a type of primary adrenal insufficiency (PAI), is an autosomal recessive disorder, known as isolated glucocorticoid deficiency or hereditary unresponsiveness to adrenocorticotropic hormone (ACTH) occur during early childhood and neonatal periods [1, 2].