Le et al. (2017) in a study involving six DS subjects with SCN1A‐negative identified one subject presenting a de novo heterozygous missense novel variant c.695G>A (p.Arg232Gln) in GABRB3. These authors reviewed 13 cases of EEs from the literature correlated to GABRB3 mutation with a total of 12 variants. Here, GABRB3 is linked to Dravet syndrome.