Variants in PSORS1C3 have been associated with the risk of allopurinol-, carbamazepine-, and phenytoin-induced SJS/TEN hypersensitivity reactions52 and MICA encodes the protein MHC class I polypeptide-related sequence A53 which has been implicated in immune surveillance.54 The gene discussed is MICA; the disease is Schwartz-Jampel syndrome.