In one female, after a subtotal resection of the paraspinal tumour diagnosed as neuroblastoma differentiating type, n-myc (−), chemotherapy was used (etoposide + carboplatin/cyclophosphamide + doxorubicin + vincristine), which resulted in a complete resolution of OMS and a complete remission unconfirmed (Cru) of the malignancy. Here, MYCN is linked to opsoclonus-myoclonus syndrome.