The MYH14 gene was reported to be related to peripheral neuropathy, myopathy, hoarseness and hearing loss (PNMHH) [6], and the MYH14 protein is expressed widely within cochlear tissues, such as the organ of Corti, spiral prominence epithelium, stria vascularis, and cochlear duct. This evidence concerns the gene MYH14 and peripheral neuropathy-myopathy-hoarseness-hearing loss syndrome.