SPSS is distinguished by the presence of multiple eyelid cysts, while OODD is apparently characterised by hypoplasia of lingual papillae.4,8 In the present study, we found homozygote or heterozygote missense mutation c.682T>A (p.F228I) in the WNT10A gene of six affected members of the family with oligodontia without any ectodermal features. The gene discussed is WNT10A; the disease is Oligodontia.