There were 3 studies investigating an association between HLA-A*1101 and CM-induced SJS/TEN with SOC in Japanese, Brazilian and Indian populations.23,33,34 The numbers of subjects carrying at least one allele of HLA-A*1101 were 17 out of 213 in cases and 144 out of 822 in controls.23,33,34 The overall OR was 0.43 (95% CI = 0.24–0.76). This evidence concerns the gene HLA-A and Schwartz-Jampel syndrome.