DMD and deafness: Mutations in families with DFNX3 deafness might occur in a novel gene located within the Xp21.2 locus (Lalwani et al., 1994), however, among families previously reported as having segregating HI that mapped to the DMD locus (Xp21.2), none presented with any of the typical clinical signs of DMD (Lalwani et al., 1994; Pfister et al., 1999).