Glutaric acidemia I (GA-I) is an autosomal recessive metabolic disorder of lysine, hydroxylysine, and tryptophan metabolism caused by a deficiency of the Glutaryl-CoA Dehydrogenase (GCDH) enzyme (Hedlund et al., 2006). This evidence concerns the gene GCDH and glutaryl-CoA dehydrogenase deficiency.