This observation is in line with several DICER1-related primitive neoplasms that recapitulate the organ of origin, a finding reflected in the predominance of the “blastoma” terminologies (pleuropulmonary blastoma, pineoblastoma, pituitary blastoma, and others) for several DICER1-related malignancies [17, 18, 32]. This evidence concerns the gene DICER1 and pineoblastoma.