ITGAE and enteropathy-associated T-cell lymphoma: EATL represents a rare form of non-Hodgkin lymphoma that accounts for only approximately 1% of all reported cases.[5] The tumor cells in EATL are morphologically diverse, are medium to large in size, have round or polygonal nuclei, and have prominent nucleoli.[6] The immunophenotype includes the following biomarker expression pattern: CD43+, TIA-1+, CD3+, CD5–, CD7+, CD8±, CD4–, CD103+, and TCR±.