Interestingly, EGFR KDD has recently been reported in a 5-month-old male with CCSK [18], another type of pediatric renal tumor usually driven by BCOR ITD, BCOR-CCNB3 fusion or YWHAE-NUTM2 fusion [19], but none of which was detected in this case. Here, CCNB3 is linked to clear cell sarcoma of kidney.