The characteristic DSRCT immunophenotype is the coexpression of epithelial, mesenchymal, and neuroendocrine markers.13 Furthermore, the small round cells in our material were focal positive for desmin and Wilms tumor 1 (WT-1) genes and were negative for chromogranin, among others, thus helping our pathologist to distinguish DSRCT from other forms of small round cell tumors (e.g., ovarian small cell carcinoma of hypercalcemic type). Here, DES is linked to desmoplastic small round cell tumor.