The genes other than Dst-e that cause EBS are keratin 14 (Bonifas et al., 1991; Coulombe et al., 1991), keratin 5 (Lane et al., 1992) and plectin (Chavanas et al., 1996; Gache et al., 1996; McLean et al., 1996). Here, KRT14 is linked to epidermolysis bullosa simplex.