The dominant MyHCIIa myopathy, alternatively called “autosomal dominant myopathy with congenital joint contractures, ophthalmoplegia and rimmed vacuoles”, (OMIM#605637) or “Hereditary inclusion body myopathy type 3” (IBM3) starts prenatally with congenital contractures that may reverse in childhood and patients may eventually lose ambulation [30]. This evidence concerns the gene MYH2 and myopathy.