Null and hypomorphic mutations in the Golgi vesicle-tethering factor Golgi microtubule-associated protein of 210 kDa [GMAP-210; also known as thyroid hormone receptor interactor 11 (TRIP11)] are responsible for the lethal skeletal dysplasia achondrogenesis type 1A (ACG1A) and the milder odontochondrodysplasia (ODCD), respectively (Smits et al., 2010; Wehrle et al., 2019). The gene discussed is TRIP11; the disease is odontochondrodysplasia 1.