POGLUT1 and muscular dystrophy: Indeed, an abnormal somite formation has been observed in Poglut1 knockout mice [21], and we have recently shown that a reduced enzymatic activity of POGLUT1 in satellite cells, the stem cells of muscles, leads to a reduced Notch signaling, resulting in the aberrant maintenance and differentiation of satellite cells, which induces muscular dystrophy [51,52].