TLR4 and glycogen storage disease VI: The expression of TLR4 in non-classical monocytes was higher in patients with active disease and prednisone use in comparison to healthy donors (1598 AU (954–2243 AU) vs 281 AU (237–353 AU), P < 0.0001); as well as in those with active disease without prednisone treatment (1293 AU (1006–1896 AU) vs 281 AU (237–353 AU), P = 0.007) and those with complete clinical response without prednisone use (1243 AU (1118–1580 AU) vs 281 AU (237–353 AU), P = 0.023).