AGPAT2 and Berardinelli-Seip congenital lipodystrophy: BSCL is classified in four different subtypes (8); BSCL type 1 is an autosomal recessive disease due to variants (9) of the gene coding for the enzyme 1-acylglycerol-3phosphate-O-acyltransferase β (lysophosphatidic acid acyltransferase beta or AGPAT2 OMIM# 608594).