ASPS is a rare histology, characterised by a specific molecular change [t(X;17)(p11;q25) translocation, resulting in an ASPL-TFE3 gene fusion] [21], and is known to have an indolent clinical course in the non-metastatic stage, however characterized by late metastases with a 5-year OS of 20% at the metastatic stage [22, 23]. This evidence concerns the gene TFE3 and alveolar soft part sarcoma.