In eight recessive probands, bi‐allelic mutations, confirmed by parental genotyping, were identified in known deafness genes OTOF (603,681),CDH23 (601,067),PCDH15 (605,514),ADGRV1 (602,851),PDZD7 (612,971),KARS (601,421),OTOG (604,487), andGRXCR2 (615,762) (n = 1 each, Table 1). Here, CDH23 is linked to deafness.