CDH23 and deafness: With regard to the responsible gene, the most frequent causative gene was GJB2 (29%), followed by SLC26A4 (9%), CDH23 (7%), MYO7A (4%), OTOF (5%), MYO15A (3%), and LOXHD1 (2%), indicating that these deafness genes are typical deafness genes found in the prelingual CI/EAS patients.