DCTN1‐related dHMN, also known as dHNM type 7B, presents with distal limb dystrophy and weakness appearing at early adulthood,6 whereas Perry syndrome is characterized by middle‐age‐onset parkinsonism, depression, weight loss, and central hypoventilation.4, 7, 8 Recently, frontotemporal dementia (FTD) has also been considered as one of the phenotypes,9 indicating the DCTN1‐related spectrum is still expanding. Here, DCTN1 is linked to distal hereditary motor neuropathy.