THBD and hemolytic-uremic syndrome: Although preliminary, these results could provide the rationale for the use of ART-123, a human recombinant thrombomodulin tested in the setting of disseminated intravascular coagulation (without improvement of all-cause mortality) [195] and acute exacerbations of idiopathic pulmonary fibrosis (ongoing, NCT02739165), in STEC-HUS.