NR4A3 and extraskeletal myxoid chondrosarcoma: EMC is an extremely rare subtype of vulvar sarcoma that is consistently positive for vimentin, variable positivity for S100 protein, neuron-specific enolase and synaptophysin, completely negative for CK [10–16], and harhor EWSR1-NR4A3 fusion in about 65% of cases [17].