Although she was diagnosed as having interstitial lung disease-associated pSS based on the results of high-resolution computed tomography and bronchoalveolar lavage studies (increased lymphocytes without any findings suggestive of infection or malignancy), the reticular shadows and elevated serum KL-6 level improved spontaneously and no respiratory symptoms became evident, and therefore she had been followed up without steroid therapy. This evidence concerns the gene MUC1 and peeling skin syndrome.