TMEM127 and pheochromocytoma: We present a woman with the pathogenic variant c.86delG (p.Arg29Leu<i>f</i>s<sup>∗</sup>52) in the <i>TMEM127</i> gene, which has not been previously reported, associated to a bilateral phaeochromocytoma, with an uncommon initial clinical presentation and a biochemical profile that is distinctly adrenergic.