A pattern of selective muscle involvement, i.e., the concentric fatty infiltration pattern, appears to be distinctive for sarcoglycanopathies, because it was observed in most patients with various sarcoglycanopathies, including the most severely affected patients, consistent with the previously reported pattern observed in LGMD2C–2F proposed by Tasca et al. [5] and was also noted in other reports of LGMD2C [23] and LGMD2D [20, 24]. This evidence concerns the gene SGCG and sarcoglycanopathy.