Pyogenic sterile arthritis, pyoderma gangrenosum and acne (PAPA)Syndromic forms of pyoderma gangrenosumDeficiency of IL-1 receptor antagonist (DIRA)Deficiency of IL-36 receptor antagonist (DITRA)CARD-14 mediated psoriasis (CAMPS)Majeed syndromePyrin-associated autoinflammation with neutrophilic dermatosis (PAAND)Singleton-Merten syndrome (SMS)ADAM17 deficiencyAP1S3 and autoinflammatory psoriasisNFKB1-associated sterile familial autoinflammatory necrotizing fasciitis (FANF). The gene discussed is ADAM17; the disease is Smith-Magenis syndrome.