The frequencies of HLA-A*02:06:01-HLA-B*35:01:01 (Pc = 2.28 × 10−3, OR = 4.55), HLA-B*46:01:01-HLA-C*01:02:01 (Pc = 0.0099, OR = 2.62), HLA-A*02:06:01-HLA-C*01:02:01 (Pc = 2.19 × 10−4, OR = 7.43), HLA-A*02:06:01-HLA-C*03:03:01 (Pc = 0.0193, OR = 3.83), and HLA-A*02:06:01-HLA-C*03:04:01 (Pc = 0.0169, OR = 4.23) were significantly increased in CM-SJS/TEN with SOCs. Here, HLA-C is linked to Schwartz-Jampel syndrome.