Recently, it was also found that IPF patients show an abnormal expression of C-X-C motif chemokine ligand 13 (CXCL13), which is a critical chemokine for the homing of B cells and T follicular helper cells (Tfh cells) to lymphoid tissues as well as inflammatory foci [10–12]. This evidence concerns the gene CXCL13 and idiopathic pulmonary fibrosis.