This study verifies the fact, collected by other authors around the world, that pathogenic variants in WNT10A, EDAR, and EDA are the most frequently known causes of autosomal recessive hypodontia/oligodontia, autosomal recessive HED, X-linked HED, and X-linked isolated tooth agenesis. Here, EDA is linked to hypohidrotic ectodermal dysplasia.