Hypertriglyceridemia, which is not associated withincreased cholesterol, seen in 51.6% of our patients, is partof the HLH picture and can itself be a cause of pancreatitis.This is due to the action of TNF‐α and Il-1 released byactivated macrophages and inhibiting lipoprotein lipase.It is usual to observe liver abnormalities with elevatedaminotransferases, alkaline phosphatases, bilirubin, anda moderate decrease in factor V, which indicates somedegree of hepatic failure [11]. The gene discussed is LPL; the disease is liver failure.