Previous studies have reported that meningioma is a marker ofdisease severity in NF2, being associated with a 2.5- fold greater risk of mortalityas compared with NF2 patients without meningiomas.13 The patient in our case was not offered treatment because, after 2 years offollow-up, she had no new symptoms and the mass was still of almost the same size.In a word, the prognosis of ectopic meningioma appears to be good, with an overallmedian survival of 28 years. This evidence concerns the gene NF2 and meningioma.