DSP and familial dilated cardiomyopathy: Patients affected bydesmoplakin (DSP) or FLNC truncating variants,for instance, may be affected by a form of ACM with exclusive left ventricleinvolvement.20,50,51 There are several reports of DCM-patients affected bymutations in desmosomal genes that do not fulfil any (or only some) of thearrhythmogenic right ventricular dysplasia diagnostic criteria.50-52