KCNQ3 and Seizure: When compared to KCNQ2, pathogenic variants in KCNQ3 have been more rarely described, mostly in families affected with familial forms of benign epilepsies with seizures starting in the neonatal (BFNS)6, 12, 13 or early‐infantile (benign familial infantile seizures, BFIS) period.14, 15 Fewer than twenty families with BFNS and three families with BFIS with a heterozygous KCNQ3 pathogenic variant have been reported to date.16 In addition, de novo variants in KCNQ3 have been described in few children with EOEE,17, 18, 19, 20 ID apparently without epilepsy,21, 22 and cortical visual impairment.23