SMARCB1 and neoplasm: Among these new tumor variants, such as NUT-rearranged carcinoma [3, 4], HPV-related adenoid cystic-like carcinoma [5, 6], and adamantinoma-like Ewing sarcoma [7], SMARCB1-deficient sinonasal carcinoma (SDSC) stands out given its aggressiveness in the face of multimodal therapy.