Platyspondyly, a hallmark of “spondylo”-dysplasia, has never been recognized in B4GALT7-spEDS and B3GAT3-related disorders, except in the patient reported by Alazami et al. [26], whereas it is frequently reported either in B3GALT6- and SLC39A13-spEDS or in SOS, whereas in DBDQ2 it was recognized in five out of the nine investigated patients. The gene discussed is B3GALT6; the disease is Platyspondyly.